Sesiones
miércoles, febrero 25, 2009, 09:08 AM
KLIPPEL-FEIL SYNDROME ASSOCIATED WITH POSTERIOR FOSSA DERMOID CYST. CASE REPORT. JOSÉ M. GONZÁLEZ-DARDER*, ROSANA FELIU-TATAY*, JOSÉ V. PESUDO-MARTÍNEZ*, JOSÉ M. VERA-ROMÁN+
Departments of Neurosurgery* and Pathology+, Hospital General de Castellón, Castellón, Spain
Publisher in NEUROLOGICAL RESEARCH (Neurol. Res. 2002 Jul; 24(5):501-4)
Abstract
A patient with association of Klippel-Feil syndrome and posterior fossa dermoid cyst is presented. The patient, a 36 year-old man, presented with an acute obstructive hydrocephalus due to the cyst and exhibited the typical triad of the Klippel-Feil abnormality with short neck, low hairline implantation and limited neck motion along with a complex cervical vertebrae fusion. The anatomical and clinical features as well as the pathophysiology of this rare association are discussed after a review of the literature.